Authors
Davletshina L.M 1, 2, Zagidullina A.Sh.1, Batyrshin R.A.1
1 Bashkir State Medical University, Ufa
2 Clinical Emergency Hospital, Ufa
Abstract
The Sturge-Weber syndrome presented in the article in a 54 year old woman is a clinical case of sporadic encephalotrigeminal angiomatosis with ophthalmological manifestations in the form of secondary open-angle glaucoma, detected at a late stage. Primary treatment with complaints from the organ of vision made it possible to be set the main diagnosis and prescribe local antihypertensive and general syndromic treatment.
Keywords: Sturge-Weber syndrome, secondary glaucoma, phakomatosis, encephalotrigeminal angiomatosis, case report.
References
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