Authors
Ablitsov A.Y., Levchuk A.L., Ablitsov Y.A., Lovtsevich N.V., Plotnitskiy A.V., Shepetkova L.V., Sharova I.O., Suslov R.P.
Pirogov National Medical and Surgical Center, Moscow
Abstract
A case of successful surgical treatment of a patient with a giant solitary fibrous pleural tumor is presented in a clinical observation. The Doege-Potter syndrome and Pierre Marie-Bamberger syndrome, one of the manifestations of which are changes in the fingers of the «drumsticks» type, and hypoglycemia, are paraneoplastic syndromes characteristic of solitary fibrous pleural tumors (SFPT). SFPT are extremely rare. It is even rarer to find in the literature descriptions of patients with both benign and malignant SFPT and paraneoplastic syndromes, and all the authors have experience of 1–2 operations. The patient underwent a lower lobectomy on the left along with the bulk of the tumor. The operation was accompanied by massive blood loss. The postoperative period was difficult and was accompanied by complications. However, at the control examination after 8 months, the condition is satisfactory. There were no attacks of hypoglycemia after surgery, the fingers of the hands changed. No recurrence or metastasis of the tumor was detected during X-ray examination.
Keywords: zase report, Doege–Potter syndrome, hypoglycemia, solitary fibrous tumor.
References
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